| CDBP00430 | OGDH | 7p14-p13 | 2-oxoglutarate dehydrogenase, mitochondrial | Enzyme | 10 |
| CDBP04292 | OGDHL | | 2-oxoglutarate dehydrogenase-like, mitochondrial | Enzyme | 10 |
| CDBP04293 | OXGR1 | 13q32.1 | 2-oxoglutarate receptor 1 | Receptor | 1 |
| CDBP00294 | BCKDHA | 19q13.1-q13.2 | 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial | Enzyme | 12 |
| CDBP00293 | BCKDHB | 6q14.1 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial | Enzyme | 11 |
| CDBP02462 | CYP39A1 | 6p21.1-p11.2 | 24-hydroxycholesterol 7-alpha-hydroxylase | Enzyme | 5 |
| CDBP01510 | CYP7B1 | 8q21.3 | 25-hydroxycholesterol 7-alpha-hydroxylase | Enzyme | 6 |
| CDBP00979 | CYP27B1 | 12q13.1-q13.3 | 25-hydroxyvitamin D-1 alpha hydroxylase, mitochondrial | Enzyme | 7 |
| CDBP02428 | HSD3B7 | 16p11.2 | 3 beta-hydroxysteroid dehydrogenase type 7 | Enzyme | 3 |
| CDBP02411 | HSD3B1 | 1p13.1 | 3 beta-hydroxysteroid dehydrogenase/Delta 5-->4-isomerase type 1 | Enzyme | 3 |
| CDBP02412 | HSD3B2 | 1p13.1 | 3 beta-hydroxysteroid dehydrogenase/Delta 5-->4-isomerase type 2 | Enzyme | 5 |
| CDBP00336 | BPNT1 | 1q41 | 3'(2'),5'-bisphosphate nucleotidase 1 | Enzyme | 6 |
| CDBP04033 | ERI1 | 8p23.1 | 3'-5' exoribonuclease 1 | Enzyme | 1 |
| CDBP00892 | EBP | Xp11.23-p11.22 | 3-beta-hydroxysteroid-Delta(8),Delta(7)-isomerase | Enzyme | 7 |
| CDBP00853 | HMGCR | 5q13.3-q14 | 3-hydroxy-3-methylglutaryl-coenzyme A reductase | Enzyme | 6 |
| CDBP00371 | HSD17B10 | Xp11.2 | 3-hydroxyacyl-CoA dehydrogenase type-2 | Enzyme | 6 |
| CDBP01061 | HAAO | 2p21 | 3-hydroxyanthranilate 3,4-dioxygenase | Enzyme | 2 |
| CDBP02502 | BDH2 | 4q24 | 3-hydroxybutyrate dehydrogenase type 2 | Enzyme | 4 |
| CDBP00387 | HIBADH | 7p15.2 | 3-hydroxyisobutyrate dehydrogenase, mitochondrial | Enzyme | 5 |
| CDBP02423 | HIBCH | 2q32.2 | 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial | Enzyme | 7 |
| CDBP02429 | HMGCLL1 | 6p12.1 | 3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic | Enzyme | 3 |
| CDBP00793 | HSD17B7 | 1q23 | 3-keto-steroid reductase | Enzyme | 12 |
| CDBP00031 | ACAA2 | 18q21.1 | 3-ketoacyl-CoA thiolase, mitochondrial | Enzyme | 9 |
| CDBP00043 | ACAA1 | 3p22.2 | 3-ketoacyl-CoA thiolase, peroxisomal | Enzyme | 8 |
| CDBP02216 | KDSR | 18q21.3 | 3-ketodihydrosphingosine reductase | Enzyme | 5 |