| CDBP00017 | 5-aminolevulinate synthase, erythroid-specific, mitochondrial | P22557 | ALAS2 | Xp11.21 | Enzyme | Not Available |
| CDBP00022 | 5-aminolevulinate synthase, nonspecific, mitochondrial | P13196 | ALAS1 | 3p21.1 | Enzyme | Not Available |
| CDBP00047 | 2-amino-3-ketobutyrate coenzyme A ligase, mitochondrial | O75600 | GCAT | 22q13.1 | Enzyme | Not Available |
| CDBP00183 | Methylenetetrahydrofolate reductase | P42898 | MTHFR | 1p36.3 | Enzyme | Not Available |
| CDBP00242 | 4-aminobutyrate aminotransferase, mitochondrial | P80404 | ABAT | 16p13.2 | Enzyme | Not Available |
| CDBP00271 | Tyrosine aminotransferase | P17735 | TAT | 16q22.1 | Enzyme | Not Available |
| CDBP00272 | Aromatic-L-amino-acid decarboxylase | P20711 | DDC | 7p12.2 | Enzyme | Not Available |
| CDBP00277 | Aspartate aminotransferase, cytoplasmic | P17174 | GOT1 | 10q24.1-q25.1 | Enzyme | Not Available |
| CDBP00278 | Aspartate aminotransferase, mitochondrial | P00505 | GOT2 | 16q21 | Enzyme | Not Available |
| CDBP00295 | Branched-chain-amino-acid aminotransferase, cytosolic | P54687 | BCAT1 | 12p12.1 | Enzyme | Not Available |
| CDBP00319 | Kynureninase | Q16719 | KYNU | 2q22.2 | Enzyme | Not Available |
| CDBP00322 | Glucose-6-phosphate 1-dehydrogenase | P11413 | G6PD | Xq28 | Enzyme | Not Available |
| CDBP00362 | Glycogen phosphorylase, liver form | P06737 | PYGL | 14q21-q22 | Enzyme | Not Available |
| CDBP00365 | Glycogen phosphorylase, muscle form | P11217 | PYGM | 11q12-q13.2 | Enzyme | Not Available |
| CDBP00367 | Glycogen phosphorylase, brain form | P11216 | PYGB | 20p11.21 | Enzyme | Not Available |
| CDBP00370 | Kynurenine/alpha-aminoadipate aminotransferase, mitochondrial | Q8N5Z0 | AADAT | 4q33 | Enzyme | Not Available |
| CDBP00388 | Alanine--glyoxylate aminotransferase 2, mitochondrial | Q9BYV1 | AGXT2 | 5p13 | Enzyme | Not Available |
| CDBP00392 | Ornithine aminotransferase, mitochondrial | P04181 | OAT | 10q26 | Enzyme | Not Available |
| CDBP00448 | Kynurenine--oxoglutarate transaminase 1 | Q16773 | CCBL1 | 9q34.11 | Enzyme | Not Available |
| CDBP00494 | Branched-chain-amino-acid aminotransferase, mitochondrial | O15382 | BCAT2 | 19q13 | Enzyme | Not Available |
| CDBP00511 | Cystathionine gamma-lyase | P32929 | CTH | 1p31.1 | Enzyme | Not Available |
| CDBP00635 | L-serine dehydratase/L-threonine deaminase | P20132 | SDS | 12q24.13 | Enzyme | Not Available |
| CDBP00638 | Pyridoxine-5'-phosphate oxidase | Q9NVS9 | PNPO | 17q21.32 | Enzyme | Not Available |
| CDBP00650 | Formimidoyltransferase-cyclodeaminase | O95954 | FTCD | 21q22.3 | Enzyme | Not Available |
| CDBP00666 | Glutamate decarboxylase 2 | Q05329 | GAD2 | 10p11.23 | Enzyme | Not Available |