| CDBP02541 | ABHD4 | 14q11.2 | Abhydrolase domain-containing protein 4 | Enzyme | 16 |
| CDBP05038 | ABI1 | 10p11.2 | Abl interactor 1 | Enzyme | 3 |
| CDBP05007 | ACAD11 | 3q22.1 | ACAD11 protein | Enzyme | 5 |
| CDBP02400 | AACS | 12q24.31 | Acetoacetyl-CoA synthetase | Enzyme | 6 |
| CDBP02600 | ILVBL | 19p13.1 | Acetolactate synthase-like protein | Enzyme | 6 |
| CDBP00013 | ACAT2 | 6q25.3 | Acetyl-CoA acetyltransferase, cytosolic | Enzyme | 3 |
| CDBP00036 | ACAT1 | 11q22.3 | Acetyl-CoA acetyltransferase, mitochondrial | Enzyme | 3 |
| CDBP00045 | ACACA | 17q21 | Acetyl-CoA carboxylase 1 | Enzyme | 6 |
| CDBP00018 | ACACB | 12q24.11 | Acetyl-CoA carboxylase 2 | Enzyme | 6 |
| CDBP00040 | ACSS1 | 20p11.23-p11.21 | Acetyl-coenzyme A synthetase 2-like, mitochondrial | Enzyme | 6 |
| CDBP00035 | ACSS2 | 20q11.22 | Acetyl-coenzyme A synthetase, cytoplasmic | Enzyme | 6 |
| CDBP02203 | SLC33A1 | 3q25.31 | Acetyl-coenzyme A transporter 1 | Enzyme | 1 |
| CDBP00498 | ACHE | 7q22 | Acetylcholinesterase | Enzyme | 16 |
| CDBP00098 | ASMT | Xp22.3 or Yp11.3 | Acetylserotonin O-methyltransferase | Enzyme | 2 |
| CDBP01018 | ASAH1 | 8p22 | Acid ceramidase | Enzyme | 6 |
| CDBP04994 | ACPL2 | 3q23 | Acid phosphatase-like protein 2 | Enzyme | 5 |
| CDBP00966 | CHIA | | Acidic mammalian chitinase | Enzyme | 1 |
| CDBP00688 | ACO2 | 22q13.2 | Aconitate hydratase, mitochondrial | Enzyme | 4 |
| CDBP02624 | ACSS2 | 20q11.22 | ACSS2 protein | Enzyme | 6 |
| CDBP01261 | TNK2 | 3q29 | Activated CDC42 kinase 1 | Enzyme | 3 |
| CDBP05171 | ASCC3 | 6q16 | Activating signal cointegrator 1 complex subunit 3 | Transcription Factor | 3 |
| CDBP05157 | AICDA | 12p13 | Activation-induced cytidine deaminase | Enzyme | 3 |
| CDBP03512 | ABR | 17p13.3 | Active breakpoint cluster region-related protein | Enzyme | 1 |
| CDBP01104 | ACVR1 | 2q23-q24 | Activin receptor type-1 | Receptor | 5 |
| CDBP01310 | ACVR1B | 12q13 | Activin receptor type-1B | Receptor | 4 |