| CDBP00012 | Pyruvate dehydrogenase E1 component subunit beta, mitochondrial | P11177 | PDHB | 3p21.1-p14.2 | Enzyme | Not Available |
| CDBP00019 | Pyruvate carboxylase, mitochondrial | P11498 | PC | 11q13.4-q13.5 | Enzyme | Not Available |
| CDBP00044 | Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial | P08559 | PDHA1 | Xp22.1 | Enzyme | Not Available |
| CDBP00048 | Pyruvate dehydrogenase E1 component subunit alpha, testis-specific form, mitochondrial | P29803 | PDHA2 | 4q22-q23 | Enzyme | Not Available |
| CDBP00052 | Dihydrolipoyl dehydrogenase, mitochondrial | P09622 | DLD | 7q31-q32 | Enzyme | Not Available |
| CDBP00053 | Dihydrolipoyllysine-residue acetyltransferase component of pyruvate dehydrogenase complex, mitochondrial | P10515 | DLAT | 11q23.1 | Enzyme | Not Available |
| CDBP00201 | D-amino-acid oxidase | P14920 | DAO | 12q24 | Enzyme | Not Available |
| CDBP00242 | 4-aminobutyrate aminotransferase, mitochondrial | P80404 | ABAT | 16p13.2 | Enzyme | Not Available |
| CDBP00388 | Alanine--glyoxylate aminotransferase 2, mitochondrial | Q9BYV1 | AGXT2 | 5p13 | Enzyme | Not Available |
| CDBP00411 | S-adenosylmethionine decarboxylase proenzyme | P17707 | AMD1 | 6q21 | Enzyme | Not Available |
| CDBP00448 | Kynurenine--oxoglutarate transaminase 1 | Q16773 | CCBL1 | 9q34.11 | Enzyme | Not Available |
| CDBP00511 | Cystathionine gamma-lyase | P32929 | CTH | 1p31.1 | Enzyme | Not Available |
| CDBP00635 | L-serine dehydratase/L-threonine deaminase | P20132 | SDS | 12q24.13 | Enzyme | Not Available |
| CDBP00668 | Adenylate cyclase type 7 | P51828 | ADCY7 | 16q12.1 | Enzyme | Not Available |
| CDBP00669 | Adenylate cyclase type 4 | Q8NFM4 | ADCY4 | 14q12 | Enzyme | Not Available |
| CDBP00670 | Adenylate cyclase type 6 | O43306 | ADCY6 | 12q12-q13 | Enzyme | Not Available |
| CDBP00671 | Adenylate cyclase type 5 | O95622 | ADCY5 | 3q21.1 | Enzyme | Not Available |
| CDBP00672 | Adenylate cyclase type 8 | P40145 | ADCY8 | 8q24 | Enzyme | Not Available |
| CDBP00673 | Adenylate cyclase type 9 | O60503 | ADCY9 | 16p13.3 | Enzyme | Not Available |
| CDBP00674 | Adenylate cyclase type 3 | O60266 | ADCY3 | 2p23.3 | Enzyme | Not Available |
| CDBP00675 | Adenylate cyclase type 1 | Q08828 | ADCY1 | 7p13-p12 | Enzyme | Not Available |
| CDBP00710 | Pyruvate kinase isozymes M1/M2 | P14618 | PKM | 15q22 | Enzyme | Not Available |
| CDBP00712 | Pyruvate kinase isozymes R/L | P30613 | PKLR | 1q21 | Enzyme | Not Available |
| CDBP00726 | 3-mercaptopyruvate sulfurtransferase | P25325 | MPST | 22q13.1 | Enzyme | Not Available |
| CDBP00734 | Serine--pyruvate aminotransferase | P21549 | AGXT | 2q37.3 | Enzyme | Not Available |