| CDBP01243 | ABL2 | 1q25.2 | Tyrosine-protein kinase ABL2 | Enzyme | 4 |
| CDBP01034 | ABO | 9q34.2 | Histo-blood group ABO system transferase | Enzyme | 2 |
| CDBP00382 | ABP1 | 7q36.1 | Amiloride-sensitive amine oxidase [copper-containing] | Enzyme | 17 |
| CDBP03512 | ABR | 17p13.3 | Active breakpoint cluster region-related protein | Enzyme | 1 |
| CDBP00043 | ACAA1 | 3p22.2 | 3-ketoacyl-CoA thiolase, peroxisomal | Enzyme | 8 |
| CDBP00031 | ACAA2 | 18q21.1 | 3-ketoacyl-CoA thiolase, mitochondrial | Enzyme | 9 |
| CDBP00045 | ACACA | 17q21 | Acetyl-CoA carboxylase 1 | Enzyme | 6 |
| CDBP00018 | ACACB | 12q24.11 | Acetyl-CoA carboxylase 2 | Enzyme | 6 |
| CDBP02308 | ACAD10 | 12q24.12 | Acyl-CoA dehydrogenase family member 10 | Enzyme | 5 |
| CDBP02313 | ACAD11 | 3q22.1 | Acyl-CoA dehydrogenase family member 11 | Enzyme | 5 |
| CDBP05007 | ACAD11 | 3q22.1 | ACAD11 protein | Enzyme | 5 |
| CDBP02439 | ACAD8 | 11q25 | Isobutyryl-CoA dehydrogenase, mitochondrial | Enzyme | 6 |
| CDBP02440 | ACAD9 | 3q21.3 | Acyl-CoA dehydrogenase family member 9, mitochondrial | Enzyme | 6 |
| CDBP00099 | ACADL | 2q34 | Long-chain specific acyl-CoA dehydrogenase, mitochondrial | Enzyme | 8 |
| CDBP00101 | ACADM | 1p31 | Medium-chain specific acyl-CoA dehydrogenase, mitochondrial | Enzyme | 9 |
| CDBP00100 | ACADS | 12q24.31 | Short-chain specific acyl-CoA dehydrogenase, mitochondrial | Enzyme | 11 |
| CDBP01496 | ACADSB | 10q26.13 | Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial | Enzyme | 10 |
| CDBP03473 | ACADVL | 17p13.1 | Very long-chain specific acyl-CoA dehydrogenase, mitochondrial | Enzyme | 8 |
| CDBP01679 | ACAN | 15q26.1 | Aggrecan core protein | Enzyme | 0 |
| CDBP03541 | ACAP1 | 17p13.1 | Arf-GAP with coiled-coil, ANK repeat and PH domain-containing protein 1 | Metal Binding | 2 |
| CDBP04968 | ACAP2 | 3q29 | Arf-GAP with coiled-coil, ANK repeat and PH domain-containing protein 2 | Metal Binding | 1 |
| CDBP00036 | ACAT1 | 11q22.3 | Acetyl-CoA acetyltransferase, mitochondrial | Enzyme | 3 |
| CDBP00013 | ACAT2 | 6q25.3 | Acetyl-CoA acetyltransferase, cytosolic | Enzyme | 3 |
| CDBP05004 | ACBD3 | 1q42.12 | Golgi resident protein GCP60 | Enzyme | 5 |
| CDBP05005 | ACBD4 | 17q21.31 | Acyl-CoA-binding domain-containing protein 4 | Enzyme | 5 |