| CDBP00151 | ALDH4A1 | 1p36 | Delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial | Enzyme | 9 |
| CDBP00152 | NDUFA7 | 19p13.2 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 7 | Enzyme | 5 |
| CDBP00153 | TXNRD2 | 22q11.21 | Thioredoxin reductase 2, mitochondrial | Enzyme | 6 |
| CDBP00154 | NDUFA2 | 5q31 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 2 | Enzyme | 5 |
| CDBP00155 | MTR | 1q43 | Methionine synthase | Enzyme | 10 |
| CDBP00156 | MAOB | Xp11.23 | Amine oxidase [flavin-containing] B | Enzyme | 15 |
| CDBP00157 | NDUFS1 | 2q33-q34 | NADH-ubiquinone oxidoreductase 75 kDa subunit, mitochondrial | Enzyme | 6 |
| CDBP00158 | NDUFB5 | 3q26.33 | NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 5, mitochondrial | Enzyme | 5 |
| CDBP00159 | ACOX2 | 3p14.3 | Peroxisomal acyl-coenzyme A oxidase 2 | Enzyme | 7 |
| CDBP00160 | FMO4 | 1q24.3 | Dimethylaniline monooxygenase [N-oxide-forming] 4 | Enzyme | 6 |
| CDBP00161 | IVD | 15q14-q15 | Isovaleryl-CoA dehydrogenase, mitochondrial | Enzyme | 7 |
| CDBP00162 | ENPP2 | 8q24.1 | Ectonucleotide pyrophosphatase/phosphodiesterase family member 2 | Enzyme | 4 |
| CDBP00163 | NDUFC1 | 4q31.1 | NADH dehydrogenase [ubiquinone] 1 subunit C1, mitochondrial | Enzyme | 1 |
| CDBP00164 | MAOA | Xp11.3 | Amine oxidase [flavin-containing] A | Enzyme | 16 |
| CDBP00165 | NDUFC2 | 11q14.1 | NADH dehydrogenase [ubiquinone] 1 subunit C2 | Enzyme | 5 |
| CDBP00166 | FMO3 | 1q24.3 | Dimethylaniline monooxygenase [N-oxide-forming] 3 | Enzyme | 6 |
| CDBP00167 | NDUFB3 | 2q31.3 | NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 3 | Enzyme | 5 |
| CDBP00168 | NDUFB7 | 19p13.12 | NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 7 | Enzyme | 5 |
| CDBP00169 | NDUFAB1 | 16p12.2 | Acyl carrier protein, mitochondrial | Enzyme | 5 |
| CDBP00170 | NDUFA5 | 7q32 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 5 | Enzyme | 5 |
| CDBP00171 | ETFDH | 4q32-q35 | Electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial | Enzyme | 4 |
| CDBP00172 | NDUFA9 | 12p13.3 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 9, mitochondrial | Enzyme | 5 |
| CDBP00173 | MT-ND4 | | NADH-ubiquinone oxidoreductase chain 4 | Enzyme | 6 |
| CDBP00174 | SDHD | 11q23 | Succinate dehydrogenase [ubiquinone] cytochrome b small subunit, mitochondrial | Enzyme | 6 |
| CDBP00175 | NDUFS7 | 19p13.3 | NADH dehydrogenase [ubiquinone] iron-sulfur protein 7, mitochondrial | Enzyme | 6 |