| CDBP05006 | ACBD5 | 10p12.1 | Acyl-CoA-binding domain-containing protein 5 | Enzyme | 5 |
| CDBP05013 | ACBD5 | 10p12.1 | Acyl-Coenzyme A binding domain containing 5 | Enzyme | 5 |
| CDBP05011 | ACBD6 | 1q25.1 | Acyl-CoA-binding domain-containing protein 6 | Enzyme | 5 |
| CDBP05014 | ACBD7 | 10p13 | Acyl-CoA-binding domain-containing protein 7 | Enzyme | 5 |
| CDBP04244 | ACCN1 | 17q12 | Amiloride-sensitive cation channel 1, neuronal | Transporter | 0 |
| CDBP04245 | ACCN2 | 12q12 | Amiloride-sensitive cation channel 2, neuronal | Transporter | 1 |
| CDBP04246 | ACCN3 | 7q35 | Amiloride-sensitive cation channel 3 | Transporter | 1 |
| CDBP04247 | ACCN4 | 2q35 | Amiloride-sensitive cation channel 4 | Transporter | 0 |
| CDBP04248 | ACCN5 | 4q31.3-q32 | Amiloride-sensitive cation channel 5 | Transporter | 0 |
| CDBP01560 | ACE | 17q23.3 | Angiotensin-converting enzyme | Enzyme | 0 |
| CDBP03391 | ACE2 | Xp22 | Angiotensin-converting enzyme 2 | Enzyme | 2 |
| CDBP04663 | ACER1 | 19p13.3 | Alkaline ceramidase 1 | Enzyme | 6 |
| CDBP04319 | ACER2 | 9p22.1 | Alkaline ceramidase 2 | Enzyme | 6 |
| CDBP02631 | ACER3 | | Alkaline ceramidase 3 | Enzyme | 2 |
| CDBP00498 | ACHE | 7q22 | Acetylcholinesterase | Enzyme | 16 |
| CDBP00010 | ACLY | 17q21.2 | ATP-citrate synthase | Enzyme | 5 |
| CDBP00255 | ACMSD | 2q21.3 | 2-amino-3-carboxymuconate-6-semialdehyde decarboxylase | Enzyme | 1 |
| CDBP00689 | ACO1 | 9p21.1 | Cytoplasmic aconitate hydratase | Enzyme | 5 |
| CDBP00688 | ACO2 | 22q13.2 | Aconitate hydratase, mitochondrial | Enzyme | 4 |
| CDBP04988 | ACOT1 | 14q24.3 | Acyl-coenzyme A thioesterase 1 | Enzyme | 16 |
| CDBP04991 | ACOT11 | 1p32.3 | Acyl-coenzyme A thioesterase 11 | Enzyme | 5 |
| CDBP00024 | ACOT12 | 5q14.1 | Acyl-coenzyme A thioesterase 12 | Enzyme | 3 |
| CDBP00984 | ACOT2 | 14q24.3 | Acyl-coenzyme A thioesterase 2, mitochondrial | Enzyme | 16 |
| CDBP00985 | ACOT4 | 14q24.3 | Acyl-coenzyme A thioesterase 4 | Enzyme | 16 |
| CDBP05107 | ACOT6 | 14q24.3 | Putative acyl-coenzyme A thioesterase 6 | Enzyme | 1 |