| CDBP00331 | Nicotinate-nucleotide pyrophosphorylase [carboxylating] | Q15274 | QPRT | 16p11.2 | Enzyme | Not Available |
| CDBP00352 | Carbamoyl-phosphate synthase [ammonia], mitochondrial | P31327 | CPS1 | 2q35 | Enzyme | Not Available |
| CDBP00374 | Gamma-butyrobetaine dioxygenase | O75936 | BBOX1 | 11p14.2 | Enzyme | Not Available |
| CDBP00411 | S-adenosylmethionine decarboxylase proenzyme | P17707 | AMD1 | 6q21 | Enzyme | Not Available |
| CDBP00430 | 2-oxoglutarate dehydrogenase, mitochondrial | Q02218 | OGDH | 7p14-p13 | Enzyme | Not Available |
| CDBP00444 | Procollagen-lysine,2-oxoglutarate 5-dioxygenase 1 | Q02809 | PLOD1 | 1p36.22 | Enzyme | Not Available |
| CDBP00445 | Procollagen-lysine,2-oxoglutarate 5-dioxygenase 2 | O00469 | PLOD2 | 3q24 | Enzyme | Not Available |
| CDBP00446 | Procollagen-lysine,2-oxoglutarate 5-dioxygenase 3 | O60568 | PLOD3 | 7q22 | Enzyme | Not Available |
| CDBP00479 | Liver carboxylesterase 1 | P23141 | CES1 | 16q22.2 | Enzyme | Not Available |
| CDBP00480 | Cocaine esterase | O00748 | CES2 | 16q22.1 | Enzyme | Not Available |
| CDBP00516 | Beta-ureidopropionase | Q9UBR1 | UPB1 | 22q11.2 | Enzyme | Not Available |
| CDBP00652 | Aminomethyltransferase, mitochondrial | P48728 | AMT | 3p21.2-p21.1 | Enzyme | Not Available |
| CDBP00666 | Glutamate decarboxylase 2 | Q05329 | GAD2 | 10p11.23 | Enzyme | Not Available |
| CDBP00667 | Glutamate decarboxylase 1 | Q99259 | GAD1 | 2q31 | Enzyme | Not Available |
| CDBP00691 | Gamma-glutamyltranspeptidase 1 | P19440 | GGT1 | 22q11.23 | Enzyme | Not Available |
| CDBP00710 | Pyruvate kinase isozymes M1/M2 | P14618 | PKM | 15q22 | Enzyme | Not Available |
| CDBP00712 | Pyruvate kinase isozymes R/L | P30613 | PKLR | 1q21 | Enzyme | Not Available |
| CDBP00740 | Glycine dehydrogenase [decarboxylating], mitochondrial | P23378 | GLDC | 9p22 | Enzyme | Not Available |
| CDBP00786 | 4-hydroxyphenylpyruvate dioxygenase | P32754 | HPD | 12q24-qter | Enzyme | Not Available |
| CDBP00793 | 3-keto-steroid reductase | P56937 | HSD17B7 | 1q23 | Enzyme | Not Available |
| CDBP00802 | NADP-dependent malic enzyme | P48163 | ME1 | 6q12 | Metal Binding | Not Available |
| CDBP00804 | NADP-dependent malic enzyme, mitochondrial | Q16798 | ME3 | 11cen-q22.3 | Metal Binding | Not Available |
| CDBP00807 | NAD-dependent malic enzyme, mitochondrial | P23368 | ME2 | 18q21 | Metal Binding | Not Available |
| CDBP00828 | Histidine decarboxylase | P19113 | HDC | 15q21-q22 | Enzyme | Not Available |
| CDBP00829 | Serine palmitoyltransferase 1 | O15269 | SPTLC1 | 9q22.2 | Enzyme | Not Available |