| CDBP00012 | Pyruvate dehydrogenase E1 component subunit beta, mitochondrial | P11177 | PDHB | 3p21.1-p14.2 | Enzyme | Not Available |
| CDBP00044 | Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial | P08559 | PDHA1 | Xp22.1 | Enzyme | Not Available |
| CDBP00048 | Pyruvate dehydrogenase E1 component subunit alpha, testis-specific form, mitochondrial | P29803 | PDHA2 | 4q22-q23 | Enzyme | Not Available |
| CDBP00049 | Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial | Q02252 | ALDH6A1 | 14q24.3 | Enzyme | Not Available |
| CDBP00052 | Dihydrolipoyl dehydrogenase, mitochondrial | P09622 | DLD | 7q31-q32 | Enzyme | Not Available |
| CDBP00053 | Dihydrolipoyllysine-residue acetyltransferase component of pyruvate dehydrogenase complex, mitochondrial | P10515 | DLAT | 11q23.1 | Enzyme | Not Available |
| CDBP00071 | Aldo-keto reductase family 1 member C4 | P17516 | AKR1C4 | 10p15.1 | Enzyme | Not Available |
| CDBP00075 | 15-hydroxyprostaglandin dehydrogenase [NAD(+)] | P15428 | HPGD | 4q34-q35 | Enzyme | Not Available |
| CDBP00084 | Tyrosinase | P14679 | TYR | 11q14-q21 | Enzyme | Not Available |
| CDBP00085 | Aldose reductase | P15121 | AKR1B1 | 7q35 | Enzyme | Not Available |
| CDBP00100 | Short-chain specific acyl-CoA dehydrogenase, mitochondrial | P16219 | ACADS | 12q24.31 | Enzyme | Not Available |
| CDBP00112 | NADH-ubiquinone oxidoreductase chain 1 | P03886 | MT-ND1 | | Enzyme | Not Available |
| CDBP00113 | NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 1 | O75438 | NDUFB1 | 14q32.12 | Enzyme | Not Available |
| CDBP00114 | Ectonucleotide pyrophosphatase/phosphodiesterase family member 1 | P22413 | ENPP1 | 6q22-q23 | Enzyme | Not Available |
| CDBP00115 | NADH dehydrogenase [ubiquinone] iron-sulfur protein 2, mitochondrial | O75306 | NDUFS2 | 1q23 | Enzyme | Not Available |
| CDBP00119 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 12 | Q9UI09 | NDUFA12 | 12q22 | Enzyme | Not Available |
| CDBP00120 | NADH-cytochrome b5 reductase 3 | P00387 | CYB5R3 | 22q13.2 | Enzyme | Not Available |
| CDBP00122 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 1 | O15239 | NDUFA1 | | Enzyme | Not Available |
| CDBP00123 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 4-like 2 | Q9NRX3 | NDUFA4L2 | 12q13.3 | Enzyme | Not Available |
| CDBP00124 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 3 | O95167 | NDUFA3 | 19q13.42 | Enzyme | Not Available |
| CDBP00125 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 8 | P51970 | NDUFA8 | 9q33.2 | Enzyme | Not Available |
| CDBP00126 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 4 | O00483 | NDUFA4 | 7p21.3 | Enzyme | Not Available |
| CDBP00127 | NADH-ubiquinone oxidoreductase chain 4L | P03901 | MT-ND4L | | Enzyme | Not Available |
| CDBP00128 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 11 | Q86Y39 | NDUFA11 | 19p13.3 | Enzyme | Not Available |
| CDBP00130 | Lathosterol oxidase | O75845 | SC5DL | 11q23.3 | Enzyme | Not Available |