| CDBP00052 | Dihydrolipoyl dehydrogenase, mitochondrial | P09622 | DLD | 7q31-q32 | Enzyme | Not Available |
| CDBP00242 | 4-aminobutyrate aminotransferase, mitochondrial | P80404 | ABAT | 16p13.2 | Enzyme | Not Available |
| CDBP00264 | Phytanoyl-CoA dioxygenase, peroxisomal | O14832 | PHYH | 10p13 | Enzyme | Not Available |
| CDBP00271 | Tyrosine aminotransferase | P17735 | TAT | 16q22.1 | Enzyme | Not Available |
| CDBP00277 | Aspartate aminotransferase, cytoplasmic | P17174 | GOT1 | 10q24.1-q25.1 | Enzyme | Not Available |
| CDBP00278 | Aspartate aminotransferase, mitochondrial | P00505 | GOT2 | 16q21 | Enzyme | Not Available |
| CDBP00289 | Aldehyde dehydrogenase, mitochondrial | P05091 | ALDH2 | 12q24.2 | Enzyme | Not Available |
| CDBP00290 | Fatty aldehyde dehydrogenase | P51648 | ALDH3A2 | 17p11.2 | Enzyme | Not Available |
| CDBP00291 | Aldehyde dehydrogenase X, mitochondrial | P30837 | ALDH1B1 | 9p11.1 | Enzyme | Not Available |
| CDBP00295 | Branched-chain-amino-acid aminotransferase, cytosolic | P54687 | BCAT1 | 12p12.1 | Enzyme | Not Available |
| CDBP00296 | Prolyl 4-hydroxylase subunit alpha-2 | O15460 | P4HA2 | 5q31 | Enzyme | Not Available |
| CDBP00298 | Prolyl 4-hydroxylase subunit alpha-1 | P13674 | P4HA1 | 10q21.3-q23.1 | Enzyme | Not Available |
| CDBP00370 | Kynurenine/alpha-aminoadipate aminotransferase, mitochondrial | Q8N5Z0 | AADAT | 4q33 | Enzyme | Not Available |
| CDBP00374 | Gamma-butyrobetaine dioxygenase | O75936 | BBOX1 | 11p14.2 | Enzyme | Not Available |
| CDBP00388 | Alanine--glyoxylate aminotransferase 2, mitochondrial | Q9BYV1 | AGXT2 | 5p13 | Enzyme | Not Available |
| CDBP00392 | Ornithine aminotransferase, mitochondrial | P04181 | OAT | 10q26 | Enzyme | Not Available |
| CDBP00430 | 2-oxoglutarate dehydrogenase, mitochondrial | Q02218 | OGDH | 7p14-p13 | Enzyme | Not Available |
| CDBP00444 | Procollagen-lysine,2-oxoglutarate 5-dioxygenase 1 | Q02809 | PLOD1 | 1p36.22 | Enzyme | Not Available |
| CDBP00445 | Procollagen-lysine,2-oxoglutarate 5-dioxygenase 2 | O00469 | PLOD2 | 3q24 | Enzyme | Not Available |
| CDBP00446 | Procollagen-lysine,2-oxoglutarate 5-dioxygenase 3 | O60568 | PLOD3 | 7q22 | Enzyme | Not Available |
| CDBP00448 | Kynurenine--oxoglutarate transaminase 1 | Q16773 | CCBL1 | 9q34.11 | Enzyme | Not Available |
| CDBP00494 | Branched-chain-amino-acid aminotransferase, mitochondrial | O15382 | BCAT2 | 19q13 | Enzyme | Not Available |
| CDBP00631 | Glutamate dehydrogenase 2, mitochondrial | P49448 | GLUD2 | Xq24-q25 | Enzyme | Not Available |
| CDBP00658 | Glutamate dehydrogenase 1, mitochondrial | P00367 | GLUD1 | 10q23.3 | Enzyme | Not Available |
| CDBP00734 | Serine--pyruvate aminotransferase | P21549 | AGXT | 2q37.3 | Enzyme | Not Available |