| CDBP00116 | Succinate dehydrogenase cytochrome b560 subunit, mitochondrial | Q99643 | SDHC | 1q23.3 | Enzyme | Not Available |
| CDBP00145 | Succinate dehydrogenase [ubiquinone] flavoprotein subunit, mitochondrial | P31040 | SDHA | 5p15 | Enzyme | Not Available |
| CDBP00174 | Succinate dehydrogenase [ubiquinone] cytochrome b small subunit, mitochondrial | O14521 | SDHD | 11q23 | Enzyme | Not Available |
| CDBP00188 | Succinate dehydrogenase [ubiquinone] iron-sulfur subunit, mitochondrial | P21912 | SDHB | 1p36.1-p35 | Enzyme | Not Available |
| CDBP00243 | Succinate-semialdehyde dehydrogenase, mitochondrial | P51649 | ALDH5A1 | 6p22 | Enzyme | Not Available |
| CDBP00264 | Phytanoyl-CoA dioxygenase, peroxisomal | O14832 | PHYH | 10p13 | Enzyme | Not Available |
| CDBP00296 | Prolyl 4-hydroxylase subunit alpha-2 | O15460 | P4HA2 | 5q31 | Enzyme | Not Available |
| CDBP00298 | Prolyl 4-hydroxylase subunit alpha-1 | P13674 | P4HA1 | 10q21.3-q23.1 | Enzyme | Not Available |
| CDBP00374 | Gamma-butyrobetaine dioxygenase | O75936 | BBOX1 | 11p14.2 | Enzyme | Not Available |
| CDBP00444 | Procollagen-lysine,2-oxoglutarate 5-dioxygenase 1 | Q02809 | PLOD1 | 1p36.22 | Enzyme | Not Available |
| CDBP00445 | Procollagen-lysine,2-oxoglutarate 5-dioxygenase 2 | O00469 | PLOD2 | 3q24 | Enzyme | Not Available |
| CDBP00446 | Procollagen-lysine,2-oxoglutarate 5-dioxygenase 3 | O60568 | PLOD3 | 7q22 | Enzyme | Not Available |
| CDBP00676 | Succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial | P55809 | OXCT1 | 5p13.1 | Enzyme | Not Available |
| CDBP00678 | Succinyl-CoA:3-ketoacid coenzyme A transferase 2, mitochondrial | Q9BYC2 | OXCT2 | 1p34 | Enzyme | Not Available |
| CDBP00832 | Succinyl-CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial | P53597 | SUCLG1 | 2p11.2 | Enzyme | Not Available |
| CDBP00834 | Succinyl-CoA ligase [GDP-forming] subunit beta, mitochondrial | Q96I99 | SUCLG2 | 3p14.1 | Enzyme | Not Available |
| CDBP00909 | Succinyl-CoA ligase [ADP-forming] subunit beta, mitochondrial | Q9P2R7 | SUCLA2 | 13q12.2-q13.3 | Enzyme | Not Available |
| CDBP00959 | Aspartyl/asparaginyl beta-hydroxylase | Q12797 | ASPH | 8q12.1 | Enzyme | Not Available |
| CDBP00960 | Hypoxia-inducible factor 1-alpha inhibitor | Q9NWT6 | HIF1AN | 10q24 | Transcription Factor | Not Available |
| CDBP01484 | Mitochondrial dicarboxylate carrier | Q9UBX3 | SLC25A10 | 17q25.3 | Enzyme | Not Available |
| CDBP01943 | Solute carrier family 13 member 3 | Q8WWT9 | SLC13A3 | 20q12-q13.1 | Transporter | Not Available |
| CDBP02131 | 17-beta-hydroxysteroid dehydrogenase type 6 | O14756 | HSD17B6 | 12q13 | Enzyme | Not Available |
| CDBP02196 | Solute carrier family 13 member 1 | Q9BZW2 | SLC13A1 | 7q31-q32 | Transporter | Not Available |
| CDBP02315 | Solute carrier family 13 member 2 | Q13183 | SLC13A2 | 17p13.2 | Transporter | Not Available |
| CDBP02359 | Trimethyllysine dioxygenase, mitochondrial | Q9NVH6 | TMLHE | Xq28 | Enzyme | Not Available |