| CDBP00101 | ACADM | 1p31 | Medium-chain specific acyl-CoA dehydrogenase, mitochondrial | Enzyme | 9 |
| CDBP00102 | UCK1 | 9q34.13 | Uridine-cytidine kinase 1 | Enzyme | 14 |
| CDBP00103 | NME4 | 16p13.3 | Nucleoside diphosphate kinase, mitochondrial | Enzyme | 13 |
| CDBP00104 | RRM1 | 11p15.5 | Ribonucleoside-diphosphate reductase large subunit | Enzyme | 9 |
| CDBP00105 | NME1 | 17q21.3 | Nucleoside diphosphate kinase A | Enzyme | 14 |
| CDBP00106 | NME7 | 1q24 | Nucleoside diphosphate kinase 7 | Enzyme | 13 |
| CDBP00107 | RRM2 | 2p25-p24 | Ribonucleoside-diphosphate reductase subunit M2 | Enzyme | 9 |
| CDBP00108 | NME2 | 17q21.3 | Nucleoside diphosphate kinase B | Enzyme | 13 |
| CDBP00109 | NME3 | 16q13.3 | Nucleoside diphosphate kinase 3 | Enzyme | 13 |
| CDBP00110 | NME6 | 3p21 | Nucleoside diphosphate kinase 6 | Enzyme | 13 |
| CDBP00111 | NDUFB10 | 16p13.3 | NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 10 | Enzyme | 1 |
| CDBP00112 | MT-ND1 | | NADH-ubiquinone oxidoreductase chain 1 | Enzyme | 6 |
| CDBP00113 | NDUFB1 | 14q32.12 | NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 1 | Enzyme | 5 |
| CDBP00114 | ENPP1 | 6q22-q23 | Ectonucleotide pyrophosphatase/phosphodiesterase family member 1 | Enzyme | 13 |
| CDBP00115 | NDUFS2 | 1q23 | NADH dehydrogenase [ubiquinone] iron-sulfur protein 2, mitochondrial | Enzyme | 6 |
| CDBP00116 | SDHC | 1q23.3 | Succinate dehydrogenase cytochrome b560 subunit, mitochondrial | Enzyme | 6 |
| CDBP00117 | PIPOX | 17q11.2 | Peroxisomal sarcosine oxidase | Enzyme | 5 |
| CDBP00118 | PAOX | 10q26.3 | Peroxisomal N(1)-acetyl-spermine/spermidine oxidase | Enzyme | 7 |
| CDBP00119 | NDUFA12 | 12q22 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 12 | Enzyme | 5 |
| CDBP00120 | CYB5R3 | 22q13.2 | NADH-cytochrome b5 reductase 3 | Enzyme | 4 |
| CDBP00121 | AOX1 | 2q33 | Aldehyde oxidase | Enzyme | 11 |
| CDBP00122 | NDUFA1 | | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 1 | Enzyme | 5 |
| CDBP00123 | NDUFA4L2 | 12q13.3 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 4-like 2 | Enzyme | 5 |
| CDBP00124 | NDUFA3 | 19q13.42 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 3 | Enzyme | 5 |
| CDBP00125 | NDUFA8 | 9q33.2 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 8 | Enzyme | 5 |