| CDBP00016 | Malonyl-CoA decarboxylase, mitochondrial | O95822 | MLYCD | 16q24 | Enzyme | Not Available |
| CDBP00028 | Carnitine O-acetyltransferase | P43155 | CRAT | 9q34.1 | Enzyme | Not Available |
| CDBP00031 | 3-ketoacyl-CoA thiolase, mitochondrial | P42765 | ACAA2 | 18q21.1 | Enzyme | Not Available |
| CDBP00035 | Acetyl-coenzyme A synthetase, cytoplasmic | Q9NR19 | ACSS2 | 20q11.22 | Enzyme | Not Available |
| CDBP00040 | Acetyl-coenzyme A synthetase 2-like, mitochondrial | Q9NUB1 | ACSS1 | 20p11.23-p11.21 | Enzyme | Not Available |
| CDBP00043 | 3-ketoacyl-CoA thiolase, peroxisomal | P09110 | ACAA1 | 3p22.2 | Enzyme | Not Available |
| CDBP00046 | Trifunctional enzyme subunit beta, mitochondrial | P55084 | HADHB | 2p23 | Enzyme | Not Available |
| CDBP00049 | Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial | Q02252 | ALDH6A1 | 14q24.3 | Enzyme | Not Available |
| CDBP00099 | Long-chain specific acyl-CoA dehydrogenase, mitochondrial | P28330 | ACADL | 2q34 | Enzyme | Not Available |
| CDBP00100 | Short-chain specific acyl-CoA dehydrogenase, mitochondrial | P16219 | ACADS | 12q24.31 | Enzyme | Not Available |
| CDBP00101 | Medium-chain specific acyl-CoA dehydrogenase, mitochondrial | P11310 | ACADM | 1p31 | Enzyme | Not Available |
| CDBP00141 | Peroxisomal acyl-coenzyme A oxidase 1 | Q15067 | ACOX1 | 17q25.1 | Enzyme | Not Available |
| CDBP00159 | Peroxisomal acyl-coenzyme A oxidase 2 | Q99424 | ACOX2 | 3p14.3 | Enzyme | Not Available |
| CDBP00161 | Isovaleryl-CoA dehydrogenase, mitochondrial | P26440 | IVD | 15q14-q15 | Enzyme | Not Available |
| CDBP00187 | Peroxisomal acyl-coenzyme A oxidase 3 | O15254 | ACOX3 | 4p15.3 | Enzyme | Not Available |
| CDBP00197 | Glutaryl-CoA dehydrogenase, mitochondrial | Q92947 | GCDH | 19p13.2 | Enzyme | Not Available |
| CDBP00220 | Hepatic triacylglycerol lipase | P11150 | LIPC | 15q21-q23 | Enzyme | Not Available |
| CDBP00237 | Diacylglycerol O-acyltransferase 1 | O75907 | DGAT1 | 8q24.3 | Enzyme | Not Available |
| CDBP00252 | Propionyl-CoA carboxylase beta chain, mitochondrial | P05166 | PCCB | 3q21-q22 | Enzyme | Not Available |
| CDBP00253 | Propionyl-CoA carboxylase alpha chain, mitochondrial | P05165 | PCCA | 13q32 | Enzyme | Not Available |
| CDBP00293 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial | P21953 | BCKDHB | 6q14.1 | Enzyme | Not Available |
| CDBP00294 | 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial | P12694 | BCKDHA | 19q13.1-q13.2 | Enzyme | Not Available |
| CDBP00307 | Acyl-CoA desaturase | O00767 | SCD | 10q24.31 | Enzyme | Not Available |
| CDBP00381 | Trifunctional enzyme subunit alpha, mitochondrial | P40939 | HADHA | 2p23 | Enzyme | Not Available |
| CDBP00431 | Non-specific lipid-transfer protein | P22307 | SCP2 | 1p32 | Enzyme | Not Available |