| CDBP00151 | Delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial | P30038 | ALDH4A1 | 1p36 | Enzyme | Not Available |
| CDBP00191 | Glutathione reductase, mitochondrial | P00390 | GSR | 8p21.1 | Enzyme | Not Available |
| CDBP00208 | Glutamine--fructose-6-phosphate aminotransferase [isomerizing] 2 | O94808 | GFPT2 | 5q34-q35 | Enzyme | Not Available |
| CDBP00210 | Glutamine--fructose-6-phosphate aminotransferase [isomerizing] 1 | Q06210 | GFPT1 | 2p13 | Enzyme | Not Available |
| CDBP00242 | 4-aminobutyrate aminotransferase, mitochondrial | P80404 | ABAT | 16p13.2 | Enzyme | Not Available |
| CDBP00271 | Tyrosine aminotransferase | P17735 | TAT | 16q22.1 | Enzyme | Not Available |
| CDBP00277 | Aspartate aminotransferase, cytoplasmic | P17174 | GOT1 | 10q24.1-q25.1 | Enzyme | Not Available |
| CDBP00278 | Aspartate aminotransferase, mitochondrial | P00505 | GOT2 | 16q21 | Enzyme | Not Available |
| CDBP00295 | Branched-chain-amino-acid aminotransferase, cytosolic | P54687 | BCAT1 | 12p12.1 | Enzyme | Not Available |
| CDBP00325 | Amidophosphoribosyltransferase | Q06203 | PPAT | 4q12 | Enzyme | Not Available |
| CDBP00370 | Kynurenine/alpha-aminoadipate aminotransferase, mitochondrial | Q8N5Z0 | AADAT | 4q33 | Enzyme | Not Available |
| CDBP00388 | Alanine--glyoxylate aminotransferase 2, mitochondrial | Q9BYV1 | AGXT2 | 5p13 | Enzyme | Not Available |
| CDBP00392 | Ornithine aminotransferase, mitochondrial | P04181 | OAT | 10q26 | Enzyme | Not Available |
| CDBP00448 | Kynurenine--oxoglutarate transaminase 1 | Q16773 | CCBL1 | 9q34.11 | Enzyme | Not Available |
| CDBP00491 | Glutamate--cysteine ligase catalytic subunit | P48506 | GCLC | 6p12 | Enzyme | Not Available |
| CDBP00492 | Glutamate--cysteine ligase regulatory subunit | P48507 | GCLM | 1p22.1 | Enzyme | Not Available |
| CDBP00493 | N-acetylglutamate synthase, mitochondrial | Q8N159 | NAGS | 17q21.31 | Enzyme | Not Available |
| CDBP00494 | Branched-chain-amino-acid aminotransferase, mitochondrial | O15382 | BCAT2 | 19q13 | Enzyme | Not Available |
| CDBP00538 | Bifunctional glutamate/proline--tRNA ligase | P07814 | EPRS | 1q41 | Enzyme | Not Available |
| CDBP00552 | Asparagine synthetase [glutamine-hydrolyzing] | P08243 | ASNS | 7q21.3 | Enzyme | Not Available |
| CDBP00560 | GMP synthase [glutamine-hydrolyzing] | P49915 | GMPS | 3q24 | Enzyme | Not Available |
| CDBP00631 | Glutamate dehydrogenase 2, mitochondrial | P49448 | GLUD2 | Xq24-q25 | Enzyme | Not Available |
| CDBP00634 | Glutamine synthetase | P15104 | GLUL | 1q31 | Enzyme | Not Available |
| CDBP00639 | Glutaminase liver isoform, mitochondrial | Q9UI32 | GLS2 | 12q13 | Enzyme | Not Available |
| CDBP00640 | CTP synthase 1 | P17812 | CTPS1 | 1p34.1 | Enzyme | Not Available |