| CDBP00052 | Dihydrolipoyl dehydrogenase, mitochondrial | P09622 | DLD | 7q31-q32 | Enzyme | Not Available |
| CDBP00099 | Long-chain specific acyl-CoA dehydrogenase, mitochondrial | P28330 | ACADL | 2q34 | Enzyme | Not Available |
| CDBP00100 | Short-chain specific acyl-CoA dehydrogenase, mitochondrial | P16219 | ACADS | 12q24.31 | Enzyme | Not Available |
| CDBP00101 | Medium-chain specific acyl-CoA dehydrogenase, mitochondrial | P11310 | ACADM | 1p31 | Enzyme | Not Available |
| CDBP00112 | NADH-ubiquinone oxidoreductase chain 1 | P03886 | MT-ND1 | | Enzyme | Not Available |
| CDBP00113 | NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 1 | O75438 | NDUFB1 | 14q32.12 | Enzyme | Not Available |
| CDBP00114 | Ectonucleotide pyrophosphatase/phosphodiesterase family member 1 | P22413 | ENPP1 | 6q22-q23 | Enzyme | Not Available |
| CDBP00115 | NADH dehydrogenase [ubiquinone] iron-sulfur protein 2, mitochondrial | O75306 | NDUFS2 | 1q23 | Enzyme | Not Available |
| CDBP00116 | Succinate dehydrogenase cytochrome b560 subunit, mitochondrial | Q99643 | SDHC | 1q23.3 | Enzyme | Not Available |
| CDBP00117 | Peroxisomal sarcosine oxidase | Q9P0Z9 | PIPOX | 17q11.2 | Enzyme | Not Available |
| CDBP00118 | Peroxisomal N(1)-acetyl-spermine/spermidine oxidase | Q6QHF9 | PAOX | 10q26.3 | Enzyme | Not Available |
| CDBP00119 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 12 | Q9UI09 | NDUFA12 | 12q22 | Enzyme | Not Available |
| CDBP00120 | NADH-cytochrome b5 reductase 3 | P00387 | CYB5R3 | 22q13.2 | Enzyme | Not Available |
| CDBP00121 | Aldehyde oxidase | Q06278 | AOX1 | 2q33 | Enzyme | Not Available |
| CDBP00122 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 1 | O15239 | NDUFA1 | | Enzyme | Not Available |
| CDBP00123 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 4-like 2 | Q9NRX3 | NDUFA4L2 | 12q13.3 | Enzyme | Not Available |
| CDBP00124 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 3 | O95167 | NDUFA3 | 19q13.42 | Enzyme | Not Available |
| CDBP00125 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 8 | P51970 | NDUFA8 | 9q33.2 | Enzyme | Not Available |
| CDBP00126 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 4 | O00483 | NDUFA4 | 7p21.3 | Enzyme | Not Available |
| CDBP00127 | NADH-ubiquinone oxidoreductase chain 4L | P03901 | MT-ND4L | | Enzyme | Not Available |
| CDBP00128 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 11 | Q86Y39 | NDUFA11 | 19p13.3 | Enzyme | Not Available |
| CDBP00129 | Thioredoxin reductase 1, cytoplasmic | Q16881 | TXNRD1 | 12q23-q24.1 | Enzyme | Not Available |
| CDBP00130 | Lathosterol oxidase | O75845 | SC5DL | 11q23.3 | Enzyme | Not Available |
| CDBP00132 | NADH dehydrogenase [ubiquinone] iron-sulfur protein 4, mitochondrial | O43181 | NDUFS4 | 5q11.1 | Enzyme | Not Available |
| CDBP00133 | Ribosyldihydronicotinamide dehydrogenase [quinone] | P16083 | NQO2 | 6p25.2 | Enzyme | Not Available |